2003, Cilt 16, Sayı 1, Sayfa(lar) 045-048
SPONTANEOUS REMISSION OF NEPHROTIC SYNDROME IN HUS-TTP
Neşe Karaaslan Bıyıklı1, Harika Alpay1, Yüksel Yılmaz, Işıl Barlan
1Sub-department of Pediatric Nephrology, Department of Pediatrics, School of Medicine, Marmara University, Istanbul, Turkey
2Sub-department of Pediatric Neurology, Department of Pediatrics, School of Medicine, Marmara University, Istanbul, Turkey
3 Sub-department of Pediatric Allergy-Immunology, Department of Pediatrics, School of Medicine, Marmara University, Istanbul, Turkey
Keywords: HUS-TTP, Encephalopathy, Central nervous system involvement, Nephrotic syndrome

We report a three-year-old girl with thrombotic microangiopathy, severe encephalopathy and nephrotic syndrome. She presented with encephalopathy, oliguria and edema with laboratory findings of thrombocytopenia, anemia, heavy proteinuria, and elevated liver enzymes and blood urea nitrogen. The encephalopathy lasted for 7 days where as the nephrotic syndrome lasted for over a month. Hemolytic uremic syndrome (HUS) - thrombotic thrombocytopenic purpura (TTP) with severe neurological involvement and nephrotic syndrome that improved without any sequelae was discussed.